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Медицинские вопросы и проблемы подростков, больных муковисцидозом

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68

Ramsey BW, Davies J, McElvaney NG et al. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med 2011;365:1663-72

69

Rosenfeld M, Pepe MS, Longton G, Emerson J, FitzSimmons S, Morgan

70

Wang X, Dockery DW, Wypij D, Fay ME, Ferris BG. Pulmonary function between 6 and 18 years of age. Pediatr Pulmonol 1993; 15:75-88

71

Hankinson JL, Odencrantz JR, Fedan KB. Spirometric reference values from a sample of the general U.S. population. Am J Respir Crit Care Med 1999; 159:179-87

72

Corey M, Edwards L, Levison H, Knowles M. Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis. J Pediatr 1997;131:809-14

73

Konstan MW, Morgan WJ, Butler SM et al. Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis. J Pediatr 2007; 151:134-9

74

Konstan MW, Wagener JS, Yegin A, Millar SJ, Pasta DJ, VanDevanter DR. Design and powering of cystic fibrosis clinical trials using rate of FEV1 decline as an efficacy endpoint. J Cyst Fibros 2010; 9:332-8

75

VanDevanter DR, Wagener JS, Pasta DJ et al. Pulmonary outcome prediction (POP) tools for cystic fibrosis patients. Pediatr Pulmonol 2010;45:1156-66

76

Konstan MW, Morgan WJ, Butler SM et al. Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis. J Pediatr 2007; 151:134-9

77

Konstan MW, Wagener JS, VanDevanter DR. Characterizing aggressiveness and predicting future progression of CF lung disease. J Cyst Fibros 2009;8S:S15-S19

78

Schluchter MD, Konstan MW, Drumm ML, Yankaskas JR, Knowles MR. Classifying severity of cystic fibrosis lung disease using longitudinal pulmonary function data. Am J Respir Crit Care Med 2006; 174:7 80-6

79

Schluchter MD, Konstan MW, Drumm ML, Yankaskas JR, Knowles MR. Classifying severity of cystic fibrosis lung disease using longitudinal pulmonary function data. Am J Respir Crit Care Med 2006; 174:7 80-6

80

Konstan MW, Wagener JS, VanDevanter DR. Characterizing aggressiveness and predicting future progression of CF lung disease. J Cyst Fibros 2009;8S:S15-S19

81

Konstan MW, Morgan WJ, Butler SM et al. Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis. J Pediatr 2007; 151:134-9

82

Konstan MW, Morgan WJ, Butler SM et al. Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis. J Pediatr 2007; 151:134-9

83

Demko CA, Byard PJ, Davis PB. Gender differences in cystic fibrosis: Pseudomonas aeruginosa infection. J Clin Epidemiol 1995; 48:1041-9

84

Kristidis P Bozon D, Corey M et al. Genetic determination of exocrine pancreatic function in cystic fibrosis. Am J Hum Genet 1992;50:1178-84

85

The Cystic Fibrosis Genotype-Phenotype Consortium. Correlation between genotype and phenotype in patients with cystic fibrosis. New Engl J Med 1993; 329:1308-13

86

McKone EF, Emerson SS, Edwards KL et al. Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study. Lancet 2003; 361:1671-6

87

McKone EF, Goss CH, Aitken ML. CFTR genotype as a predictor of prognosis in cystic fibrosis. Chest 2006; 130:1441-7

88

Sanders DB, Hoffman LR, Emerson J et al. Return of FEV(1) after pulmonary exacerbation in children with cystic fibrosis. Pediatr Pulmonol 2010;45:127-34

89

Wagener JS, VanDevanter DR, Pasta DJ, Regelmann W, Morgan WJ, Konstan MW. Oral, inhaled, and intravenous antibiotic choice for treating pulmonary exacerbations in cystic fibrosis. Pediatr Pulmonol 2012. (In press) DOI: 10.1002/ ppul. 22652

90

Konstan MW, Morgan WJ, Butler SM et al. Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis. J Pediatr 2007; 151:134-9

91

Konstan MW, Butler SM, Schidlow DV, Morgan WJ, Julius JR, Johnson CA. Patterns of medical practice in cystic fibrosis: part II. Use of therapies. Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis. Pediatr Pulmonol 1999;28:248-54

92

Konstan MW, VanDevanter DR, Rasouliyan L et al. Trends in the use of routine therapies in cystic fibrosis: 1995-2005. Pediatr Pulmonol 2010; 45:1167-72

93

Dziuban EJ, Saab-Abazeed L, Chaudhry SR, Streetman DS, Nasr SZ. Identifying barriers to treatment adherence and related attitudinal patterns in adolescents with cystic fibrosis. Pediatr Pulmonol 2010; 45:450-8

94

Modi AC, Marciel KK, Slater SK, Drotar D, Quittner AQ. The influence of parental supervision on medical adherence in adolescents with cystic fibrosis: developmental shifts from pre to late adolescence. Children's Health Care 2008; 37:78-92

95

Vandenbranden SL, McMullen A, Schechter MS et al. Lung function decline from adolescence to young adulthood in cystic fibrosis. Pediatr Pulmonol 2012;47:135-43

96

Konstan MW, Byard PJ, Hoppel CL, Davis PB. Effect of high-dose ibuprofen in patients with cystic fibrosis. N Engl J Med 1995; 332:848-54

97

Lands LC, Milner R, Cantin AM, Manson D, Corey M. High-dose ibuprofen in cystic fibrosis: Canadian safety and effectiveness trial. J Pediatr 2007; 151:249-54

98

Konstan MW, Schluchter MD, Xue W, Davis PB. Clinical use of ibuprofen is associated with slower FEV1 decline in children with cystic fibrosis. Am J Respir Crit Care Med 2007;176:1084-9

99

Ren CL, Pasta DJ, Rasouliyan L, Wagener JS, Konstan MW, Morgan WJ. The initiation of inhaled corticosteroid therapy in cystic fibrosis patients is associated with a slower rate of lung function decline. J Pediatr 2008; 153:746-51

100

Konstan MW, Wagener JS, Pasta DJ et al. Clinical use of dornase alpha is associated with a slower rate of FEV1 decline in cystic fibrosis. Pediatr Pulmonol 2011;46:545-53

101

Konstan MW, Butler SM, Schidlow DV, Morgan WJ, Julius JR, Johnson CA. Patterns of medical practice in cystic fibrosis: part II. Use of therapies. Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis. Pediatr Pulmonol 1999;28:248-54

102

Konstan MW, VanDevanter DR, Rasouliyan L et al. Trends in the use of routine therapies in cystic fibrosis: 1995-2005. Pediatr Pulmonol 2010; 45:1167-72

103

Konstan MW, VanDevanter DR, Rasouliyan L et al. Trends in the use of routine therapies in cystic fibrosis: 1995-2005. Pediatr Pulmonol 2010; 45:1167-72

104

Konstan MW, Butler SM, Schidlow DV, Morgan WJ, Julius JR, Johnson CA. Patterns of medical practice in cystic fibrosis: part II. Use of therapies. Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis. Pediatr Pulmonol 1999;28:248-54

105

Martin B, Schechter MS, Jaffe A, Cooper P, Bell SC, Ranganathan S. Comparison of the US and Australian cystic fibrosis registries: the impact of newborn screening. Pediatrics 2012; 129:348-55

106

Knudson RJ, Lebowitz MD, Holberg CJ, Burrows B. Changes in the normal maximal expiratory flow-volume curve with growth and aging. Am Rev Respir Dis 1983; 127:725-34

107

Wang X, Dockery DW, Wypij D, Fay ME, Ferris BG. Pulmonary function between 6 and 18 years of age. Pediatr Pulmonol 1993; 15:75-88

108

Hankinson JL, Odencrantz JR, Fedan KB. Spirometric reference values from a sample of the general U.S. population. Am J Respir Crit Care Med 1999; 159:179-87

109

Martin B, Schechter MS, Jaffe A, Cooper P, Bell SC, Ranganathan S. Comparison of the US and Australian cystic fibrosis registries: the impact of newborn screening. Pediatrics 2012; 129:348-55

110

VanDevanter DR, Rasouliyan LH, Murphy TM et al. Trends in the clinical characteristics of the U.S. cystic fibrosis patient population from 1995 to 2005. Pediatr Pulmonol 2008; 43:739-44

111

Konstan MW, VanDevanter DR, Rasouliyan L et al. Trends in the use of routine therapies in cystic fibrosis: 1995-2005. Pediatr Pulmonol 2010; 45:1167-72

112

VanDevanter DR, Rasouliyan LH, Murphy TM et al. Trends in the clinical characteristics of the U.S. cystic fibrosis patient population from 1995 to 2005. Pediatr Pulmonol 2008; 43:739-44

113

Konstan MW, Butler SM, Schidlow DV, Morgan WJ, Julius JR, Johnson CA. Patterns of medical practice in cystic fibrosis: part II. Use of therapies. Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis. Pediatr Pulmonol 1999;28:248-54

114

Konstan MW, VanDevanter DR, Rasouliyan L et al. Trends in the use of routine therapies in cystic fibrosis: 1995-2005. Pediatr Pulmonol 2010; 45:1167-72

115

Cystic Fibrosis Foundation Patient Registry: 2010 Annual Data Report. Bethesda, MD: Cystic Fibrosis Foundation, 2011

116

Cystic Fibrosis Foundation Patient Registry: 2010 Annual Data Report. Bethesda, MD: Cystic Fibrosis Foundation, 2011

117

Konstan MW, Wagener JS, VanDevanter DR. Characterizing aggressiveness and predicting future progression of CF lung disease. J Cyst Fibros2009;8S:S15-S19

118

Konstan MW, Morgan WJ, Butler SM et al. Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis. J Pediatr 2007; 151:134-9

119

Konstan MW, VanDevanter DR, Rasouliyan L et al. Trends in the use of routine therapies in cystic fibrosis: 1995-2005. Pediatr Pulmonol 2010; 45:1167-72

120

Own SJ, Bell SC. Transition of adolescents with cystic fibrosis from paediatric to adult care. Clin Respir J 2011;5:64-75

121

Own SJ, Bell SC. Transition of adolescents with cystic fibrosis from paediatric to adult care. Clin Respir J 2011;5:64-75

122

Conway SP Transition from paediatric to adult-orientated care for adolescents with cystic fibrosis. Disabil Rehabil 1998;20:209-16

123

Schumacher KL, Meleis Al. Transition: a central concept in nursing. Image J NursSch 1994;26:119-27

124

Schumacher KL, Meleis Al. Transition: a central concept in nursing. Image J NursSch 1994;26:119-27

125

] Kralik D, Visentin K, van Loon A. Transition: a literature review. J Adv Nurs 2006; 55:320-9

126

World Health Organization. Child and adolescent health. Available at: http://www.searo.who.int/en/Section13/Section1245_4980.htm Accessed 19 September 2012

127

Conway SP Transition from paediatric to adult-orientated care for adolescents with cystic fibrosis. Disabil Rehabil 1998;20:209-16

128

Conway SP Transition from paediatric to adult-orientated care for adolescents with cystic fibrosis. Disabil Rehabil 1998;20:209-16

129

Conway SP Transition from paediatric to adult-orientated care for adolescents with cystic fibrosis. Disabil Rehabil 1998;20:209-16

130

Brumfield K, Lansbury G. Experiences of adolescents with cystic fibrosis during their transition from pediatric to adult health care: a qualitative study of young Australian adults. Disabil Rehabil 2004;26:223-34

131

Conway SP Transition from paediatric to adult-orientated care for adolescents with cystic fibrosis. Disabil Rehabil 1998;20:209-16

132

Eiser С Effects of chronic illness on children and their families. Adv Psychiatr Treat 1997; 3:204-10

133

Conway SP Transition from paediatric to adult-orientated care for adolescents with cystic fibrosis. Disabil Rehabil 1998;20:209-16

134

Kralik D, Visentin K, van Loon A. Transition: a literature review. J Adv Nurs 2006; 55:320-9

135

Cowlard J. Cystic fibrosis: transition from paediatric to adult care. Nursing Standard 2003; 18(4):39-4

136

Viner R. Transition from paediatric to adult care. Bridging the gaps or passing the buck. Arch Dis Child 1999; 81:271-5

137

Kralik D, Visentin K, van Loon A. Transition: a literature review. J Adv Nurs 2006; 55:320-9

138

Own SJ, Bell SC. Transition of adolescents with cystic fibrosis from paediatric to adult care. Clin Respir J 2011;5:64-75

139

Own SJ, Bell SC. Transition of adolescents with cystic fibrosis from paediatric to adult care. Clin Respir J 2011;5:64-75

140

Own SJ, Bell SC. Transition of adolescents with cystic fibrosis from paediatric to adult care. Clin Respir J 2011;5:64-75

141

Own SJ, Bell SC. Transition of adolescents with cystic fibrosis from paediatric to adult care. Clin Respir J 2011;5:64-75

142

Conway SP Transition from paediatric to adult-orientated care for adolescents with cystic fibrosis. Disabil Rehabil 1998;20:209-16

143

Conway SP Transition from paediatric to adult-orientated care for adolescents with cystic fibrosis. Disabil Rehabil 1998;20:209-16

144

Kerem E, Conway S, Heijerman H; Concensus Committee. Standards of care for patients with cystic fibrosis: a European consensus. J Cyst Fibros 2005;4:7-26

145

Smith LJ, McKay КО, van Asperen PR Selvadurai H, Fitzgerald DA. Normal development of the lung and premature birth. Paediatr Respir Rev 2010; 11:135-42

146

Esterly JR, Oppenheimer EH. Observations in cystic fibrosis of the pancreas. 3. Pulmonary lesions. Johns Hopkins Med J 1968; 122:94-101

147

Sturgess J, Imrie J. Quantitative evaluation of the development of tracheal submucosal glands in infants with cystic fibrosis and control infants. Am J Pathol 1982;106:303-11

148

Bedrossian CW, Greenberg SD, Singer DB, Hansen JJ, Rosenberg HS. The lung in cystic fibrosis. A quantitative study including prevalence of pathologic findings among different age groups. Hum Pathol 1976; 7:195-204

149

Chow CW, Landau LI, Taussig LM. Bronchial mucous glands in the newborn with cystic fibrosis. Eur J Pediatr 1982; 139:240-3

150

Larson JE, Delcarpio JB, Farberman MM, Morrow SL, Cohen JC. CFTR modulates lung secretory cell proliferation and differentiation. Am J Physiol Lung Cell Mol Physiol 2000; 279:L333-41

151

Davies LA, Varathalingam A, Painter H et al. Adenovirus-mediated in utero expression of CFTR does not improve survival of CFTR knockout mice. Mol Ther2008; 16:812-18

152

Weibel ER, Gomez DM. A principle for counting tissue structures on random sections. J Appl Physiol 1962; 17:343-8

153

Narayanan M, Owers-Bradley J, Beardsmore CS et al. Alveolarization continues during childhood and adolescence: new evidence from helium-3 magnetic resonance. Am J Respir Crit Care Med 2012; 185:186-91

154

Matsui H, Grubb BR, Tarran R et al. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell 1998;95:1005-15

155

Tarran R, Button B, Picher M et al. Normal and cystic fibrosis airway surface liquid homeostasis. The effects of phasic shear stress and viral infections. J Biol Chem 2005; 280:35751-9

156

de Vrankrijker AM, Wolfs TF, van der Ent CK. Challenging and emerging pathogens in cystic fibrosis. Paediatr Respir Rev 2010; 11:246-54. Zemanick ET, Sagel SD, Harris JK. The airway microbiome in cystic fibrosis and implications for treatment. Curr Opin Pediatr 2011; 23:319-24

157

Zemanick ET, Sagel SD, Harris JK. The airway microbiome in cystic fibrosis and implications for treatment. Curr Opin Pediatr 2011; 23:319-24

158

Sibley CD, Surette MG. The polymicrobial nature of airway infections in cystic fibrosis: Cangene Gold Medal Lecture. Can J Microbiol 2011;57:69-77

159

Williams HD, Davies JC. Basic science for the chest physician: Pseudomonas aeruginosa and the cystic fibrosis airway. Thorax 2012; 67:465-7

160

Stenbit AE, Flume PA. Pulmonary exacerbations in cystic fibrosis. Curr Opin Pulm Med 2011; 17:442-7

161

Asner S, Waters V, Solomon M et al. Role of respiratory viruses in pulmonary exacerbations in children with cystic fibrosis. J Cyst Fibros 2012; 11:433-9

162

Waters V, Stanojevic S, Atenafu EG et al. Effect of pulmonary exacerbations on long-term lung function decline in cystic fibrosis. Eur Respir J 2012;40:61-6

163

Sanders DB, Hoffman LR, Emerson J et al. Return of FEV1 after pulmonary exacerbation in children with cystic fibrosis. Pediatr Pulmonol 2010; 45:127-34

164

Parkins MD, Rendall JC, Elborn JS. Incidence and risk factors for pulmonary exacerbation treatment failures in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa. Chest 2012;141:485-93

165

Armstrong DS, Grimwood K, Carlin JB et al. Lower airway inflammation in infants and young children with cystic fibrosis. Am J Respir Crit Care Med 1997; 156:1197-204

166

Stoltz DA, Meyerholz DK, Pezzulo AA et al. Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth. Sci Transl Med 2010;2:29-31

167

Muhlebach MS, Stewart PW, Leigh MW, Noah TL. Quantitation of inflammatory responses to bacteria in young cystic fibrosis and control patients. Am J Respir Crit Care Med 1999;160:186-91

168

Saiman L, Prince A. Pseudomonas aeruginosa pili bind to asialo GM1 which is increased on the surface of cystic fibrosis epithelial cells. J Clin Invest 1993;92:1875-80

169

RatnerAJ, Bryan R, Weber A et al. Cystic fibrosis pathogens activate Ca2+-dependent mitogen-activated protein kinase signaling pathways in airway epithelial cells. J Biol Chem 2001;276:19267-75

170

Knorre A, Wagner M, Schaefer HE, Colledge WH, Pahl HL. DeltaF508-CFTR causes constitutive NF-kappaB activation through an ER-overload response in cystic fibrosis lungs. Biol Chem 2002;383:271-82

171

Bonfield TL, Konstan MW, Burfeind P Panuska JR, Hilliard JB, Berger M. Normal bronchial epithelial cells constitutively produce the antiinflammatory cytokine interleukin-10, which is downregulated in cystic fibrosis. Am J Respir Cell Mol Biol 1995;13:257-61

172

Karp CL, Flick LM, Park KW et al. Defective lipoxin-mediated antiinflammatory activity in the cystic fibrosis airway. Nat Immunol 2004; 5:388-92

173

Moriceau S, Lenoir G, Witko-Sarsat V. In cystic fibrosis homozygotes and heterozygotes, neutrophil apoptosis is delayed and modulated by diamide or roscovitine: evidence for an innate neutrophil disturbance. J Innate Immun 2010; 2:260-6

174

Hayes E, Pohl K, McElvaney NG, Reeves EF1 The cystic fibrosis neutrophil: a specialized yet potentially defective cell. Arch Immunol Ther Exp 2011; 59:97-112

175

Hartl D, Latzin P Hordijk P et al. Cleavage of CXCR1 on neutrophils disables bacterial killing in cystic fibrosis lung disease. Nat Med 2007; 13:1423-30

176

Griese M, Kappler M, Gaggar A, Hartl D. Inhibition of airway proteases in cystic fibrosis lung disease. Eur Respir J 2008;32:783-95

177

Hilliard TN, Regamey N, Shute JK et al. Airway remodelling in children with cystic fibrosis. Thorax 2007; 62:1074-80

178

Regamey N, Ochs M, Hilliard TN et al. Increased airway smooth muscle mass in children with asthma, cystic fibrosis, and non-cystic fibrosis bronchiectasis. Am J Respir Crit Care Med 2008; 177:837-13

179

Laguna ТА, Wagner BD, Starcher В et al. Urinary desmosine: a biomarker of structural lung injury during CF pulmonary exacerbation. Pediatr Pulmonol 2012;47:856-63

180

Regamey N, Tsartsali L, Hilliard TN et al. Distinct patterns of inflammation in the airway lumen and bronchial mucosa of children with cystic fibrosis. Thorax 2012; 67:164-70

181

Tan HL, Regamey N, Brown S, Bush A, Lloyd CM, Davies JC. The Th17 pathway in cystic fibrosis lung disease. Am J Respir Crit Care Med 2011; 184:252-8

182

Xiao H, Li DX, Liu M. Knowledge translation: airway epithelial cell migration and respiratory diseases. Cell Mol Life Sci 2012. (In press) DOI: 10.1007/s00018-012-1044-z

183

Crosby LM, Waters CM. Epithelial repair mechanisms in the lung. Am J Physiol Lung Cell Mol Physiol 2010;298:L715-31

184

Rock JR, Hogan BL. Epithelial progenitor cells in lung development, maintenance, repair, and disease. Annu Rev Cell Dev Biol 2011; 27:493-512

185

Hegab AE, Ha VL, Gilbert JL et al. Novel stem/progenitor cell population from murine tracheal submucosal gland ducts with multipotent regenerative potential. Stem Cells 2011; 29:1283-93

186

Hong KU, Reynolds SD, Giangreco A, Hurley CM, Stripp BR. Clara cell secretory protein-expressing cells of the airway neuroepithelial body microenvironment include a label-retaining subset and are critical for epithelial renewal after progenitor cell depletion. Am J Respir Cell Mol Biol 2001; 24:671-81

187

Fujino N, Kubo H, Suzuki T et al. Isolation of alveolar epithelial type II progenitor cells from adult human lungs. Lab Invest 2011; 91:363-78

188

Krause DS. Bone marrow-derived lung epithelial cells. Proc Am Thorac Soc 2008; 5:699-702

189

Legrand C, Gilles C, Zahm JM et al. Airway epithelial cell migration dynamics. MMP-9 role in cell-extracellular matrix remodeling. J Cell Biol 1999;146:517-29

190

Legrand C, Polette M, Tournier JM et al. uPA/plasmin system-mediated MMP-9 activation is implicated in bronchial epithelial cell migration. Exp Cell Res 2001; 264:326-36

191

Xiao H, Li DX, Liu M. Knowledge translation: airway epithelial cell migration and respiratory diseases. Cell Mol Life Sci 2012. (In press) DOI: 10.1007/s00018-012-1044-z

192

Hajj R, Lesimple P Nawrocki-Raby B, Birembaut P Puchelle E, Coraux С Human airway surface epithelial regeneration is delayed and abnormal in cystic fibrosis. J Pathol 2007;211:340-50

193

Trinh NT, Prive A, Maille E, Noel J, Brochiero E. EGF and K+ channel activity control normal and cystic fibrosis bronchial epithelia repair. Am J Physiol Lung Cell Mol Physiol 2008; 295:L866-80

194

Trinh NT Bardou O, Prive A et al. Improvement of defective cystic fibrosis airway epithelial wound repair after CFTR rescue. Eur Respir J 2012. (In press) DOI: 10.1183/09031936.00221711

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